01 June 2002
A case of Hughes-Stovin syndrome associated with Budd-Chiari syndrome
Rosa Daniela Grembiale, Massimo Calderazzo, Girolamo Pelaia, Andrea Gallelli, Fernando Roccia, Giuseppe Vero, Saverio Naty, Rosario MaselliCase Rep Clin Pract Rev 2002; 3(2):92-94 :: ID: 474541
Abstract
Background: Hughes-Stovin syndrome, currently classified as a miscellaneous vasculitis, consists of one or more pulmonary artery aneurysms associated with systemic venous thrombosis. The evolution of this rare disease is commonly characterized by the rupture of the aneurysms, often responsible for a fatal fulminant hemoptysis.
Case report: Our case report refers to a young man complaining of a severe hemoptysis, who presented with a pulmonary artery aneurysm that was revealed by computed chest tomography; therefore, he underwent a right
lower lobectomy. Afew years later, an acute encephalopathy occurred, which was associated with the development of abdominal collateral blood flow and esophagogastric varices; magnetic resonance imaging showed
a thrombotic occlusion of inferior vena cava.
Conclusions: These findings suggested the diagnosis of Hughes-Stovin syndrome associated with Budd-Chiari syndrome.
Keywords: Hughes-Stovin syndrome, Budd-Chiari syndrome
49
In Press
17 Mar 2024 : Case report
Rare Presentation of Rapidly Involuting Congenital Hemangioma of the Skull: A Case ReportAm J Case Rep In Press; DOI: 10.12659/AJCR.943370
18 Mar 2024 : Case report
Perineal Benign Symmetric Lipomatosis in a Female Patient: A Case ReportAm J Case Rep In Press; DOI: 10.12659/AJCR.943803
18 Mar 2024 : Case report
Successful Endovascular Microembolization for Post-Traumatic High-Flow Priapism: A Case ReportAm J Case Rep In Press; DOI: 10.12659/AJCR.943467
19 Mar 2024 : Case report
Jejunal Diverticulosis Causing Small Intestinal Volvulus and Closed Loop ObstructionAm J Case Rep In Press; DOI: 10.12659/AJCR.943376
Most Viewed Current Articles
07 Mar 2024 : Case report
Neurocysticercosis Presenting as Migraine in the United StatesDOI :10.12659/AJCR.943133
Am J Case Rep 2024; 25:e943133
10 Jan 2022 : Case report
A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...DOI :10.12659/AJCR.935263
Am J Case Rep 2022; 23:e935263
19 Jul 2022 : Case report
Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19DOI :10.12659/AJCR.936128
Am J Case Rep 2022; 23:e936128
23 Feb 2022 : Case report
Penile Necrosis Associated with Local Intravenous Injection of CocaineDOI :10.12659/AJCR.935250
Am J Case Rep 2022; 23:e935250