18 January 2022>: Articles
A 34-Year-Old Thai Man Presenting with Pulmonary Stenosis and Heart Failure 24 Years After Surgical Correction with the Rastelli Procedure for Congenital Dextro-Transposition of the Great Artery, Ventricular Septal Defect, and Pulmonary Atresia
Challenging differential diagnosis, Congenital defects / diseases
Natnicha Pongbangli A* , Sasivimon Jai-aue D , Wannaphorn Rotchanapanya E , Wanwarang Wongcharoen DDOI: 10.12659/AJCR.933078
Am J Case Rep 2022; 23:e933078
Figure 5. (A–C) The right-left heart catheterization in our patient demonstrated a high right ventricular systolic pressure of 120 mmHg compared with a left ventricular systolic pressure of 128 mmHg. The systolic pressure gradient across the right ventricle to the pulmonary artery (120 to 106 mmHg), the main pulmonary artery (106 mmHg) to both the proximal right pulmonary artery (25 mmHg) and the left pulmonary artery (73 mmHg) were also reported. These findings were compatible with significant right ventricular outflow tract obstruction and significant peripheral pulmonary stenosis. Another finding was significant oxygen step-up from right atrium to right ventricular level (63% to 71%, respectively). Therefore, either an intracardiac shunt at the ventricular level or VSD patch leakage with a left-to-right shunt was confirmed in our case.