20 April 2004
An intraabdominal desmoid tumor in a patient with familial adenomatous polyposis
Vahit Ozmen, Coskun Polat, Sezgin Yilmaz, Tolga Ozmen, Ersin SelcukCase Rep Clin Pract Rev 2004; 5(null):86-89 :: ID: 12312
Abstract
Background: Familial adenomatous polyposis is an autosomal dominant disease. It is characterized by hundreds of adenomas of the colorectal region and desmoid tumors can sometimes occur in
extracolonic manifestation of this disease.Case Report: A case of huge intraabdominal desmoid tumor invading the whole small bowel mesentery and the aorta was described. Total proctocolectomy and ileo-anal anastomosis was performed in a 42 years old woman with familial adenomatous polyposis. A huge desmoid tumor occured five years after the surgery. The tumor was 10 to 15 cm in size and multipl lymph nodes were present around it. It was originating from the mesentery of the small bowel and tightly adherent to the aorta. The frozen section of the tumor revelaed mesenchymal tumor. Estrogen receptor was positive.But the mass was considered unresectable unless the removal of the whole small intestine and the excision of the aorta were performed. vealed mesenteric fibromatosis. The patient was discharged on 4th postoperative day and then tamoxifen (20 mg daily) was prescibed. She was followed up by clinical and CT examinations. Neither clinical nor CT evidence of disease progression has been observed for eighteen months.Conclusions: This case was considered us that the progression of the desmoid tumor is affected by the hormonal influence.
Keywords: Familial adenomatous polyposis, total proctocolectomy, desmoid tumor
0
In Press
12 Feb 2024 : Case report
Diagnostic Challenges and Imaging Considerations for Intraparotid Facial Nerve Schwannoma: A Case Report an...Am J Case Rep In Press; DOI: 10.12659/AJCR.942870
12 Feb 2024 : Case report
Erdheim-Chester Disease Occult on Radiographs and CT but Visible on MRI and PETAm J Case Rep In Press; DOI: 10.12659/AJCR.941169
12 Feb 2024 : Case report
Surgical Treatment of Spontaneous Superficial Temporal Artery Arteriovenous Malformation: A Case ReportAm J Case Rep In Press; DOI: 10.12659/AJCR.942839
13 Feb 2024 : Case report
Warfarin Woes: A Rare Case of Hemoperitoneum with Intramural Small Bowel HematomaAm J Case Rep In Press; DOI: 10.12659/AJCR.943519
Most Viewed Current Articles
10 Jan 2022 : Case report
A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...DOI :10.12659/AJCR.935263
Am J Case Rep 2022; 23:e935263
19 Jul 2022 : Case report
Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19DOI :10.12659/AJCR.936128
Am J Case Rep 2022; 23:e936128
05 Mar 2022 : Case report
Acute Limb Ischemia After Self-Injection of Crushed Morphine Tablets into the Radial Artery: Role of Infrar...DOI :10.12659/AJCR.935336
Am J Case Rep 2022; 23:e935336
02 Apr 2022 : Case report
Infective Endocarditis Caused by Pseudomonas luteola in a Pediatric Patient. A Case Report and Review of Li...DOI :10.12659/AJCR.935743
Am J Case Rep 2022; 23:e935743