Elżbieta Czekajska-Chehab, Paweł Krawczyk, Marta Adamczyk-Korbel, Andrzej Drop, Janusz Milanowski
CaseRepClinPractRev 2004; 5:506-510
Background: Tracheobronchomegaly, also known as Mounier-Kuhn syndrome, is a rare congenital disorder characterised by marked dilation of the trachea and mainstem bronchi due to elastic fibres and smooth muscles atrophy. Case Report: We report here a case of a 45-year-old male patient with a ten-year history of recurrent respiratory infections and bronchiectasis that resulted in respiratory failure. The diagnosis of tracheobronchomegaly was made basing on the spiral multi-slice computed tomography (MSCT) scanning with a high resolution mode (HRCT). Conclusions: Tracheobronchomegaly should be considered as the cause of respiratory system infections and respiratory failure in young adults. While other examinations give normal results, MSCT with virtual bronchoscopy and 3D reconstructions usually enable the diagnosis to be made.
Keywords: Tracheobronchomegaly, Bronchiectasis, Mounier-Kuhn syndrome, high-resolution computed tomography, multi-slice computed tomography