01 March 2002
Case of a neonate with Cantrell’s pentalogy complicated by
necrotizing enterocolitis
Arleta Zajączkowska-Sadlok, Kazimierz Koziołkiewicz, Piotr Korbal
Case Rep Clin Pract Rev 2002; 3(1):24-27 :: ID: 475090
Abstract
Background: Cantrell’s pentalogy is a rare congenital defect syndrome, including hernia of the umbilical cord, diaphragmatic defect, abnormalities of the sternum structure, pericardial defect and heart defect. Only 6 cases
of children with the above syndrome who survived were described before 1996. Now, advances in intensive care and new surgical techniques allow to correct more congenital defects, thus making possible further development
of the child.
Case report: The paper presents a case of a neonate, born after full-term pregnancy, operated on on the first day of life because of omphalocele, in whom detection of other anomalies contributed to the diagnosis of Cantrell’s
pentalogy with complex heart defect in the form of Fallot’s tetralogy. The post-operative course was additionally complicated by necrotizing enterocolitis, requiring exteriorization of the small intestine and long-term complete
parenteral feeding. The enterostomy was closed in the 2nd month of life. Because of retardation of psychomotor development, due probably to numerous repeated hospitalizations, the child underwent rehabilitation according to Vojta’s method, which resulted in gradual development of motor and cognitive functions. The patient required close co-operation between the parents and physicians representing many medical disciplines.
Cardiosurgical consultation led to qualification of the boy for surgical correction of heart defects which is to be performed at the age of 1 year. Then the patient is scheduled for reconstruction of the abdominal integument.
Conclusions: Therefore, Cantrell’s pentalogy seems to be one of the defect syndromes, in which survival and nearly normal development of the child is possible owing to advances in pediatric surgery, intensive care and
therapy.
Keywords: pentalogy of Cantrell, necrotizing enterocolitis, hernia of umbilical cord
31
In Press
12 Mar 2024 : Case report
Successful Treatment of Lithium-Induced Nephrogenic Diabetes Insipidus with Celecoxib: A Promising Therapeu...Am J Case Rep In Press; DOI: 10.12659/AJCR.943244
13 Mar 2024 : Case report
Recurrent Marginal Zone Lymphoma with Bone Marrow Involvement Detected by ¹⁸F-FDG PET/CT and Biopsy: A Diag...Am J Case Rep In Press; DOI: 10.12659/AJCR.943275
13 Mar 2024 : Case report
Unveiling the Temporal Aspect of MRI Tattoo Reactions: A Prospective Evaluation of a Newly-Acquired Tattoo ...Am J Case Rep In Press; DOI: 10.12659/AJCR.943411
13 Mar 2024 : Case report
Cardiac and Intramuscular Metastases Following Nephroureterectomy for Metachronous Urothelial CarcinomaAm J Case Rep In Press; DOI: 10.12659/AJCR.942864
Most Viewed Current Articles
07 Mar 2024 : Case report
Neurocysticercosis Presenting as Migraine in the United StatesDOI :10.12659/AJCR.943133
Am J Case Rep 2024; 25:e943133
10 Jan 2022 : Case report
A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...DOI :10.12659/AJCR.935263
Am J Case Rep 2022; 23:e935263
19 Jul 2022 : Case report
Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19DOI :10.12659/AJCR.936128
Am J Case Rep 2022; 23:e936128
23 Feb 2022 : Case report
Penile Necrosis Associated with Local Intravenous Injection of CocaineDOI :10.12659/AJCR.935250
Am J Case Rep 2022; 23:e935250