24 November 2021: Articles
Successful One-and-a-Half Ventricle Repair of Right Ventricle Dysfunction Due to Lymphoblastic Leukemia Treatment in a Patient with Restrictive Cardiomyopathy
Unusual setting of medical care, Rare disease
Mikhail Ramazovich Chiaureli A , Dmitry Victorovich Kovalev D , Ivan Aleksandrovich Yurlov C , Anton Vladimirovich Minaev B* , Vladimir Petrovich Podzolkov FDOI: 10.12659/AJCR.933677
Am J Case Rep 2021; 22:e933677
Table 1. Surgical treatment of acquired severe right ventricular dysfunction of non-congenital ethiology by BDCA.
| Author | Diagnosis | Age/sex | RA/RV | Function of RV | TV regurgitation | Pressure, mm Hg | Surgery | Result |
|---|---|---|---|---|---|---|---|---|
| Gorgulu S. et al., 200 5 | ARVD | 16/F | Dilated/dilated | Severe RV systolic dysfunction | Severe | PA - 23/5 (10) | BDCA + TV annuloplasty by DeVega | At discharge the cyanosis disappeared, the O2 saturation increased from 87 to 97% |
| Vaidyanathan S. et al., 2017 | ARVD | 26/F | Dilated/dilated | Severe RV systolic dysfunction | Normal | PA - 20/6 (11) | Glenn shunt | At discharge saturation improved from 80 to 89%.Patient is asymptomaticat 18-month follow-up: no ventricular arrhythmia |
| Anbarasu M. et al., 2004 | RV EMF | 27/M | Enlargement/obliteration of RV apex and a discrete shelf at the infundibulum causing RVOT obstruction | RV function was normal | Moderate | PA - 20/14 (15) | Endocardial shelf removed, outflow, widened with a patch of pericardium+TV annuloplasty by DeVega+BDCA | At discharge no systemic desaturation, improvement in RV size, mild tricuspid regurgitation |
| Mishra A. et al., 2002 | RV EMF | 25/M | Gross enlargement/severe RV endomyo-cardial fibrosis with severe obliteration of the RV cavity and apex | N/A | Severe | RA - 25 RV end-diastolic - 24 | BDCA | The postoperative recovery was stormy. After 8 years of follow-up, he was in NYHA FC II and back at work. Echocardiography showed an EF of 71%, no progression of disease |
| ARVD – arrhythmogenic right ventricular dysplasia; RV EMF – right ventricular endomyocardial fibrosis; F – female; M – male; RV – right ventricle; TV – tricuspid valve; RA – right atrium; EF – ejection fraction; PA – pulmonary artery; BDCA – bidirectional cavopulmonary anastomosis; N/A – not applicable. | ||||||||