Erdheim-Chester Disease with Renal Mass Presentation: Report of the First Case From Palestine and a Review of the Literature

17 November 2023: Articles

Rare disease

Hanood Bassam Abu Rass ^A* , Mohammad Abuawad ^D* , Yazan Abueideh ^A , Ezzideen Luai Malhis ^A

DOI: 10.12659/AJCR.941912

Am J Case Rep 2023; 24:e941912

Table 3. Abnormal CT scan findings.

Kidneys	Bilateral hairy kidney signFew bilateral cortical cysts with calcified wallsRight renal mass
Aorta	Coated aorta sign
Heart	Mild pericardial effusion
Bone	Osteolytic lesion in T12 (D12) and Sclerotic lesion in right iliac bone
Liver	Hepatomegaly
Ureter	Involvement of the proximal ureter
^* Coated aorta sign is a radiological sign in Erdheim-Chester disease for circumferential infiltration of the aorta, which is the most characteristic cardiovascular finding of Erdheim-Chester disease and can be detectable in a CT scan.